No paralogue variants have been mapped to residue 564 for KCNQ1.
KCNQ1 | KPYDVRDVIEQYSQGHLNLMVRIKELQRRL>D<QSIGKPSLFIS-----------V------- | 576 |
KCNQ2 | RPYDVMDVIEQYSAGHLDMLSRIKSLQSRV>D<QIVGRGPAITD--KDR--T--KG------- | 607 |
KCNQ3 | RPYDVKDVIEQYSAGHLDMLSRIKYLQTRI>D<MIFTPGPPSTP--KHKKSQKGSAFTFPSQQ | 597 |
KCNQ4 | RPYDVKDVIEQYSAGHLDMLGRIKSLQTRV>D<QIVGRGPGDRKAREKG--D--KG------- | 603 |
KCNQ5 | RPYDVKDVIEQYSAGHLDMLCRIKSLQTRV>D<QILGKGQITSD-KKSR--E--KI------- | 590 |
KCNA1 | ------------------------------>-<------------------------------ | |
KCNA10 | ------------------------------>-<------------------------------ | |
KCNA2 | ------------------------------>-<------------------------------ | |
KCNA3 | ------------------------------>-<------------------------------ | |
KCNA4 | ------------------------------>-<------------------------------ | |
KCNA5 | ------------------------------>-<------------------------------ | |
KCNA6 | ------------------------------>-<------------------------------ | |
KCNA7 | ------------------------------>-<------------------------------ | |
KCNB1 | PLLPVLGMYHDPLRNRGSAAAAVAGLECA->-<------------------------------ | 711 |
KCNB2 | TARPLPVTTADFSLTTPQHISTILLEETP->-<------------------------------ | 761 |
KCNC1 | GMRK----------DLCKESP---VIAKY->-<------------------------------ | 576 |
KCNC2 | GIRKG----YEKSRSLNNIAGLAGNALRL->-<------------------------------ | 614 |
KCNC3 | SIRKATGAPPLPPQDWRKPGPPS-FLPDL->-<------------------------------ | 747 |
KCNC4 | SVRKG----TFVLRDLPLQHSP---EAAC->-<------------------------------ | 624 |
KCND1 | HAPQSRSSLNAKPHDSLDLNCDSRDFVAA->-<------------------------------ | 597 |
KCND2 | PLSNSRSSLNAKMEECVKLNCEQPYVTTA->-<------------------------------ | 596 |
KCND3 | SLTTSRSSLNLKADDGLRPNCKTSQITTA->-<------------------------------ | 613 |
KCNF1 | ------------------------------>-<------------------------------ | |
KCNG1 | ------------------------------>-<------------------------------ | |
KCNG2 | ------------------------------>-<------------------------------ | |
KCNG3 | ------------------------------>-<------------------------------ | |
KCNG4 | ------------------------------>-<------------------------------ | |
KCNS1 | ------------------------------>-<------------------------------ | |
KCNS2 | ------------------------------>-<------------------------------ | |
KCNS3 | ------------------------------>-<------------------------------ | |
KCNV1 | ------------------------------>-<------------------------------ | |
KCNV2 | ------------------------------>-<------------------------------ | |
cons | > < |
Protein | CDS | Disease Classification | Disease | dbSNP links | Effect Prediction |
---|---|---|---|---|---|
p.D564N | c.1690G>A | Putative Benign | SIFT: Polyphen: | ||
p.D564H | c.1690G>C | Inherited Arrhythmia | LQTS | SIFT: Polyphen: | |
Reports | Inherited Arrhythmia | LQTS | Asymmetry of parental origin in long QT syndrome: preferential maternal transmission of KCNQ1 variants linked to channel dysfunction. Eur J Hum Genet. 2016 24(8):1160-6. doi: 10.1038/ejhg.2015.257. 26669661 |